朱婷,顾莺,胡静,陶金好,沈伟杰,杨玉霞.1例线粒体脑肌病合并呼吸衰竭危重患儿的护理[J].上海护理,2024,24(8):
1例线粒体脑肌病合并呼吸衰竭危重患儿的护理
Nursing care of a critically ill child with mitochondrial encephalomyopathy complicated with respiratory failure
投稿时间:2023-08-15  修订日期:2024-03-21
DOI:
中文关键词:  线粒体脑肌病  呼吸衰竭  儿童  护理
英文关键词:mitochondrial encephalomyopathy  respiratory failure  children  nursing
基金项目:2022年度市级医院诊疗技术推广及优化管理项目(原临床科技创新项目)(SHDC22022221);2021年上海市医苑新星青年医学人才培养资助计划(沪卫人事[2022]65号)
作者单位E-mail
朱婷 复旦大学附属儿科医院 重症医学科 695591403@qq.com 
顾莺 复旦大学附属儿科医院 护理部[]  
胡静 复旦大学附属儿科医院 护理部[]  
陶金好 复旦大学附属儿科医院 重症医学科  
沈伟杰 复旦大学附属儿科医院 重症医学科  
杨玉霞* 复旦大学附属儿科医院 重症医学科 yangyu_xia@126.com 
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中文摘要:
      【】 总结1例线粒体脑肌病合并呼吸衰竭危重患儿的护理经验。护理要点包括长期机械通气集束化护理、能量合剂药物的用药护理、合理营养支持、早期康复锻炼、暴露性角膜炎的预防及处理、全程医疗游戏辅导、个性化出院指导、遗传咨询管理。经过87天的精心治疗和照护,患儿病情好转出院,随访2个月,恢复良好。
英文摘要:
      【】 To summarize the nursing experience of a critically ill children with mitochondrial encephalomyopathy complicated with respiratory failure. The main points of nursing include bundle care of prolonged mechanic ventilation, medication nursing of energy mixture drugs, reasonable nutrition support, early rehabilitation exercise, prevention and treatment of exposure keratitis, whole medical game coaching, personalized discharge guidance, genetic counseling management. After 87 days of careful treatment and care, the patient"s condition improved and was discharged from the hospital. After 2 months of follow-up, he recovered well.
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